Atypical variant guillain-barré syndrome: case report assisted in the university hospital of manaus-am

Authors

  • Evellyn Kiyoku UFAM/HUGV
  • Ronaldo Marques Pontes Rabelo UFAM
  • Denis Birman UFAM
  • Karoliny da Silveira Vieira UEA
  • Massanobu Takatani UFAM
  • Nise Alessandra de Carvalho Souza UFAM

DOI:

https://doi.org/10.60104/revhugv9983

Keywords:

Guillain-Barre Syndrome - Paraparesis - Myelitis

Abstract

The Guillain-Barre syndrome (GBS) is a self-limiting acute polyradiculoneuritis, an increase of up to two months, secondary to bacterial or viral infection or vaccination, whose pathology shows demyelinating lesion or, more rarely, axon, the nerve roots and peripheral nerves in any topography, since cranial nerves to the lumbosacral spinal cord. The classic form is characterized by tetraparesia, up arreflexia, often associated with sensory and autonomic dysfunction symptoms, including involving the diaphragm. The albuminocytologic dissociation found in cerebrospinal fluid confirms the diagnosis and is present in 90% of cases. The treatment consists of multidisciplinary support and, for some patients, intravenous immunoglobulin or plasmapheresis. This report aims to describe a patient who was hospitalized at Hospital Universitário Getúlio Vargas (HUGV), who presented GBS with unusual clinical consisting of urinary retention, paraparesis crural, painful anesthesia in the lower limbs, and hipopalestesia below vertebra (T6), simulating spinal cord injury, with protein-cytological dissociation without changes in imaging, which showed partial improvement after receiving intravenous immunoglobulin.

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Published

2021-11-22

Issue

Section

Relato de Caso