Miastenia Gravis em Adolescente: Relato de Caso
Myasthenia Gravis in Adolescent: Case Report
Keywords:
Myasthenia gravis. Respiratory failure. Myasthenic crisis. Adolescents. Treatment.Abstract
Myasthenia gravis is an autoimmune disease of the motor plate, characterized by weakness and fatigue of the muscle. It is more common in women and has a bimodal distribution: 10-30 years and 50-70 years. Can be presented in two ways: just ocular or generalized involvement. The clinical picture is marked by preferably commitment of extraocular muscles, leading to ptosis, diploplia and ophthalmoparesis associated with muscle weakness after repetitive stimulation. In 75% of patients, the thymus is abnormal. This paper describes an adolescent who developed myasthenic crisis which endangered her life because she was unaware of the diagnosis until then. The patient came from the city of Tabatinga-AM and she was transferred to the Emergency Room South Zone in Manaus-AM with respiratory failure, and weakness of the diaphragmatic and intercostal musculature. During hospitalization and after diagnostic clarification, she showed satisfactory improvement with the use of plasmapheresis, one of the treatments of choice for this situation. This case report aims to alert the population about the medical diagnosis in adolescents, emphasizing the importance of clinical manifestations that simulate respiratory distress with non-pulmonary etiology.
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